pregnant with active HBV - tx newborn with HBIG and HBV vaccine
Beck's triad for tamponade - hypotension, JVD, muffled heart sounds (also pulsus paradoxus).
Electrical alternans
subarachnoid hemorrhage - increased ADH
...
pregnant with active HBV - tx newborn with HBIG and HBV vaccine
Beck's triad for tamponade - hypotension, JVD, muffled heart sounds (also pulsus paradoxus).
Electrical alternans
subarachnoid hemorrhage - increased ADH and BNP --> hyponatremia. Tx - water restriction
coccidioidomycosis - SW US, central/south America. Pulm infection - dry cough, weight loss,
pleuritic chest pain, erythema multiforme/nodosum, arthralgias
histoplasmosis - SE US, mid Atlantic, central US, caves. Acute PNA, but usually asymptomatic. HIV
disseminated infection- hilar LAD, pneumonitis, pancytopenia, hepatosplenomegaly, palatal ulcers.
tx- IV amphotericin B followed by lifelong itraconazole.
Blastomycosis - central US (most in Wisconsin). Often asymptomatic or flu-like Sx. Systemic
disease- lytic bone lesions, pulmonary infection, skin lesions. Dx- broad-based budding yeast. Txitraconazole, amphotericin B
aspergillosis - invasive in IMCD. CXR - cavitary lesions. CT - pulm nodules, halo sign, air crescent
sporotrichosis - subcutaneous infection. Gardeners. Travel up lymphatics for nodules on forearms
cryptococcus - pulm infection often asymptomatic. Usually meningoencephalitis in HIV with
CD4<200
hemochromatosis infections - Listeria monocytogenes, Yersinia enterocolitica, septicemia - Vibrio
vulnificusNarcolepsy treatment - methyldphenidate, modafinil, antidepressants (for cataplexy)
galactorrhea - test B-HCG, prolactin, TSH
septic abortion - cervical/blood cultures, antibiotics, gentle suction currettage
Lesch-Nyhan - x-linked recessive, HPRT deficiency, increased uric acid. Sx - self mutilation,
dystonia, spacticity, gout. Presents at 6 months.
minimal change disease - tx - prednisone, cyclophosphamide for resistant cases/frequent relapse
Sturge-Weber - seizures, retardation, trigeminal port-wine stain, hemi neuro findings, tramline
intracranial calcifications
tuberous sclerosis - seizures, retardation, intracranial calcifications (tubers), ashleaf spots,
adenoma sebaceum (red papules on face)
osteogenesis imperfecta - autosomal dominant. Type 1 collagen problem. Type 2 most severe with
perinatal fractures and often intrauterine death. Blue sclera, fractures, hypotonia, hearing loss, joint
hypermobility, dentinogenesis imperfecta
polymyalgia rheumatica - neck/shoulder/hip pain/stiffness. >50 years old, high ESR. Tx- low dose
prednisone, high dose for temporal arteritis
massive blood transfusion - citrate anticoagulant --> chelates Ca and Mg --> low Ca --> paresthesias,
hyperactive reflexes
nephrotic syndrome - dyslipidemia, accelerated atherosclerosis, hypercoagulable, risk for
MI/stroke, higher infxn susceptibility. Can have renal vein thrombosis, usually with membranous
GN
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